This silent film clip shows several victims of a disease called kuru. They are - or rather were - members of the South Fore, a tribe of approximately 8,000 people who inhabit the Okapa subdistrict of the Eastern Highlands Province of Papua New Guinea. In the 1950s and '60s, a kuru epidemic swept through the South Fore, claiming the lives of more than 1,000 members of the tribe. Later it was established that the disease was transmitted by the tribe's practice of ritualistic mortuary cannibalism.
Yuck! The word kuru means "shaking death" in the Fore language, and describes the characteristic symptoms of the disease. Because it affects mainly the cerebellum, a part of the brain involved in the co-ordination of movement, the first symptoms to manifest themselves in those infected with the disease would typically be an unsteady gait and tremors. As the disease progresses, victims become unable to stand or eat, and eventually die between 6-12 months after the symptoms first appear. Kuru belongs to a class of progressive neurodegenerative diseases called the transmissible spongiform encephalopathies (TSEs), which also includes variant Creutzfeldt-Jakob Disease (vCJD) and bovine spongiform encephalopathy (BSE, more popularly known as "Mad Cow Disease"). TSEs are fatal and infectious; in humans, they are relatively rare, and can arise sporadically, by infection, or because of genetic mutations. They are unusual in that the infectious agent which transmits the diseases is believed to a misfolded protein. (Hence, the TSEs are also referred to as the prion diseases, "prion" being a shortened form of the term "proteinaceous infectious particle").
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Following the outbreak of kuru among the Fore in the 1950s, cultural anthropologists quickly established that the disease was transmitted by the practice of mortuary cannibalism. When an individual died, the female relatives were responsible for dismembering the body. They would remove the brain, arms and feet, strip the muscle from the limbs and open the chest and abdomen to remove the internal organs. Those that died of kuru were highly regarded as sources of food, because they had layers of fat which resembled pork. It was primarily the Fore women who took part in this ritual. Often they would feed morsels of brain to young children and elderly relatives. Among the tribe, it was, therefore, women, children and the elderly who most often became infected.
Double Yuck! Seriously, I know that it's a time-honored ritual and all, but some dude in your family dies of something obvious like shaking accompanied by dementia, perhaps you might think there's something in their body causing the symptoms and just bury them. Could they have been so starved for protein? Or just mindlessly bent on following a ritual despite obvious risks? Or afraid of the consequences of not abiding? -janelane, using commonsense Update: Even granting this analysis, could they not have wanted to protect themselves? Or, will we be just as flabbergasted at ourselves in 50 years? Cannibalism & the shaking death: A new form of the disease & a possible epidemic |
